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Congenital disorders of erythropoiesis : in memory of the late Fred Stohlman / / editors, Ruth Porter, David W. Fitzsimons



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Titolo: Congenital disorders of erythropoiesis : in memory of the late Fred Stohlman / / editors, Ruth Porter, David W. Fitzsimons Visualizza cluster
Pubblicazione: Amsterdam ; ; Oxford : , : Elsevier, , 1976
Descrizione fisica: 1 online resource (418 pages) : illustrations
Soggetto topico: Erythrocytes
Blood - Diseases
Altri autori: PorterRuth  
FitzSimonsDavid W  
StohlmanFrederick  
Note generali: 'Symposium on Congenital Disorders of Erythropoiesis held at the Ciba Foundation, London, 12-14th March, 1975' - Participants.
Nota di bibliografia: Includes bibliographical references and indexes.
Nota di contenuto: Congenital Disorders of Erythropoiesis; Contents; Chairman's opening remarks; Cellular kinetics of erythropoiesis; Discussion; Regulation of fetal and adult erythropoiesis; Discussion; Embryonic erythropoiesis: some experimental systems; Discussion; Oxygen dissociation studies of red cells from chicken, mouse and human embryos; Discussion; General discussion I; Diamond-Blackfan anaemia; Discussion; Fanconi anaemia; Fanconi anaemia: cellular abnormalities and clinical predisposition to malignant disease; Discussion of the two preceding papers
Congenital dyserythropoietic anaemia type I : clinical and experimental aspects Discussion; Congenital dyserythropoietic anaemia type I1 (Hempas); Discussion; Congenital dyserythropoietic anaemias : electron microscopy; Discussion; Pathophysiology of the anaemia in thalassaemia; Discussion; The morphology and kinetics of erythropoiesis in homozygous β-thalassaemia; Discussion; The molecular defect in thalassaemia; Discussion; Cytogenetics of Fanconi anaemia and related chromosome disorders; Discussion; Fetal haemoglobin synthesis; Discussion; Regulation of globin gene expression; Discussion
General discussion II: Clinical management Conservative management; Androgen therapy in aplastic anaemia in childhood; Chelating agents; Bone marrow transplants; Genetic manipulation; Antenatal diagnosis; Concluding remarks; Index of contributors; Subject index
Titolo autorizzato: Congenital disorders of erythropoiesis  Visualizza cluster
ISBN: 1-280-78348-6
9786613693877
0-470-72019-0
0-470-71787-4
Formato: Materiale a stampa
Livello bibliografico Monografia
Lingua di pubblicazione: Inglese
Record Nr.: 9910144662403321
Lo trovi qui: Univ. Federico II
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Serie: Ciba Foundation symposium ; ; new ser. 37.