Mechanisms of ER Protein Import |
Autore | Zimmermann Richard |
Pubbl/distr/stampa | Basel, : MDPI - Multidisciplinary Digital Publishing Institute, 2022 |
Descrizione fisica | 1 electronic resource (258 p.) |
Soggetto topico |
Research & information: general
Biology, life sciences |
Soggetto non controllato |
chaperones
contact sites endoplasmic reticulum ER-SURF membrane extraction mitochondria protein targeting bimolecular luminescence complementation competition split luciferase membrane proteins protein-protein interactions Sec61 complex Sec63 synthetic peptide complementation TRAP complex ER protein translocase signal peptide protein translocation nascent peptide chain membrane insertion molecular modelling molecular dynamics simulations molecular docking signal peptidase ER translocon signal recognition particle dependent protein targeting Sec61 dependent translocation co-translational translocation inhibitor high throughput screening Sec61 Sec62 folding insertion membrane protein translocon ribosome transmembrane segment lipid droplets peroxisomes PEX3 membrane protein insertion label-free quantitative mass spectrometry differential protein abundance analysis Zellweger syndrome GET protein transport SND SRP EMC positive-inside rule hydrophobicity transmembrane helix signal recognition particle nascent polypeptide-associated complex fidelity cyclotriazadisulfonamide ER quality control DNAJC3 preprotein Sec61 translocon ribosome stalling signal sequence Sec61 translocase NAC |
Formato | Materiale a stampa ![]() |
Livello bibliografico | Monografia |
Lingua di pubblicazione | eng |
Record Nr. | UNINA-9910576886203321 |
Zimmermann Richard
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Basel, : MDPI - Multidisciplinary Digital Publishing Institute, 2022 | ||
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Lo trovi qui: Univ. Federico II | ||
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Neuromuscular Disorders in Children and Adolescents |
Autore | Korinthenberg Rudolf |
Pubbl/distr/stampa | Basel, : MDPI - Multidisciplinary Digital Publishing Institute, 2022 |
Descrizione fisica | 1 electronic resource (146 p.) |
Soggetto topico |
Medicine
Neurology & clinical neurophysiology |
Soggetto non controllato |
Pompe disease
GAA gene general population database carrier frequency genetic prevalence spinal muscular atrophy quality of life child neurology patient-reported outcomes neuromuscular carpal tunnel syndrome median nerve neuropathy electrodiagnostic studies neuromuscular ultrasound mucopolysaccharidosis neuropathy children adolescents Charcot-Marie-Tooth disease traumatic neuropathy inflammatory neuropathy metabolic neuropathy posterior spinal fusion kyphosis sagittal plane deformity signal recognition particle 3-hydroxy-3-methylglutaryl coenzyme A reductase juvenile myositis therapy clinical course chaperone-assisted autophagy clinical trials Duchenne muscular dystrophy public health surveillance distal arthrogryposis AMC ECEL1 contractures muscle MRI spinal muscular atrophy (SMA) nusinersen fine manual dexterity ultrasonographic elastography neuromuscular disease muscle brachial plexus neuritis hereditary sensory and motor neuropathy paralysis vaccination pediatrics |
Formato | Materiale a stampa ![]() |
Livello bibliografico | Monografia |
Lingua di pubblicazione | eng |
Record Nr. | UNINA-9910566465903321 |
Korinthenberg Rudolf
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Basel, : MDPI - Multidisciplinary Digital Publishing Institute, 2022 | ||
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Lo trovi qui: Univ. Federico II | ||
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