Cells and Materials for Disease Modeling and Regenerative Medicine
| Cells and Materials for Disease Modeling and Regenerative Medicine |
| Autore | Abarrategi Ander |
| Pubbl/distr/stampa | Basel, Switzerland, : MDPI - Multidisciplinary Digital Publishing Institute, 2021 |
| Descrizione fisica | 1 online resource (270 p.) |
| Soggetto topico | Research and information: general |
| Soggetto non controllato |
3D cell culture
3D models adipose tissue allografts amelogenesis biomaterials biomimicry bladder blood cancer bone and cartilage regeneration bone marrow bone tissue engineering cardiac tissue regeneration cell differentiation cementogenesis cholera toxin co-culture collagen compliance cyclic adenosine monophosphate cytokines decellularization dental pulp stem cells dentinogenesis dentogenesis devitalization disease modeling drug release materials elastin electroactive explants extracellular matrix fibrosis growth factors high hydrostatic pressure in vitro models in vivo models iPSC isoproterenol joint-on-a-chip Leigh syndrome leukemia mesenchymal stromal cells microarchitecture microenvironment mitochondrial disorder mtDNA myeloma neuron niche NSC odontogenic cells osteogenesis patterning piezoelectric psoriasis regenerative medicine rheumatoid arthritis scaffolds stem cells tissue engineering tumor-on-a-chip whole-tooth regeneration |
| Formato | Materiale a stampa |
| Livello bibliografico | Monografia |
| Lingua di pubblicazione | eng |
| Record Nr. | UNINA-9910557403303321 |
Abarrategi Ander
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| Basel, Switzerland, : MDPI - Multidisciplinary Digital Publishing Institute, 2021 | ||
| Lo trovi qui: Univ. Federico II | ||
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Lysosomal Storage Disorders: Molecular Basis and Therapeutic Approaches
| Lysosomal Storage Disorders: Molecular Basis and Therapeutic Approaches |
| Autore | Moro Enrico |
| Pubbl/distr/stampa | Basel, Switzerland, : MDPI - Multidisciplinary Digital Publishing Institute, 2021 |
| Descrizione fisica | 1 online resource (301 p.) |
| Soggetto topico | Medicine |
| Soggetto non controllato |
A4GALT
alpha-galactosidase A animal models astrogliosis autophagy axon guidance biomarkers bone involvement cathepsin D chloroquine clathrin Dkk1 dried blood spot endocytic pathways endocytosis enzyme replacement therapy exosomes experimental therapies Fabry disease GAA biomarker Gaucher disease Gaucher Disease gene therapy GLA gene globotriaosyl-sphingosine (lysoGb3) globotriaosylceramide (Gb3) globotriaosylsphingosine glycogen hematopoietic stem cell transplantations Hurler syndrome IGF2R/M6P iPSC Krabbe disease lyso-Gb3 lysosomal diseases lysosomal storage disorder lysosomal storage disorders lysosomal targeting lysosomal α-glucosidase lysosome lysosomes MIP-1β mucolipidosis II mucopolysaccharidosis IIIB mucopolysaccharidosis type I muscle NAGLU neurodegenerative disease neuronal circuit neuronopathy newborn screening Osteoimmunology Osteopontin Parkinson disease pharmacological chaperone therapy pharmacological chaperones Pompe disease precision medicine psychosine quantitative proteomics RANK/RANKL rhGAA satellite cells second tier test sortilin substrate reduction therapy tandem mass spectrometry TGF-beta Twitcher mouse variant interpretation viral vectors visual cortex visual system Wnt/β-catenin Wnt3a α-galactosidase A |
| Formato | Materiale a stampa |
| Livello bibliografico | Monografia |
| Lingua di pubblicazione | eng |
| Altri titoli varianti | Lysosomal Storage Disorders |
| Record Nr. | UNINA-9910557545503321 |
Moro Enrico
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| Basel, Switzerland, : MDPI - Multidisciplinary Digital Publishing Institute, 2021 | ||
| Lo trovi qui: Univ. Federico II | ||
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Muscle Homeostasis and Regeneration : From Molecular Mechanisms to Therapeutic Opportunities
| Muscle Homeostasis and Regeneration : From Molecular Mechanisms to Therapeutic Opportunities |
| Autore | Musarò Antonio |
| Pubbl/distr/stampa | Basel, Switzerland, : MDPI - Multidisciplinary Digital Publishing Institute, 2020 |
| Descrizione fisica | 1 online resource (500 p.) |
| Soggetto topico |
Biology, life sciences
Research and information: general |
| Soggetto non controllato |
acetylcholine receptor
Acvr1b aging atrophy biomarkers C2C12 cells calcium homeostasis cell culture cell precursors Col1a1 confocal microscopy connexin 26 connexin 43 CRISPR-Cas9 denervation differentiation Drosophila Duchenne muscular dystrophy electron microscopy evolution exercise exon deletion exosomes experimental methods extracellular vesicles FAPs fascicle fibro/adipogenic progenitors fibrosis gap junctions genetic control genetic variation genotype growth factors heavy resistance exercise heterotopic ossification hibernation Hibernation HO precursors hyperplasia hypertrophy IGF2R immunocytochemistry inflammation inflammatory response iPSC longitudinal growth lysine macrophages mass cytometry metazoans mitochondria mitochondrial dynamics mitochondrial fission mitochondrial fusion mitochondrial quality control mitochondrial-derived vesicles (MDVs) mitochondrial-lysosomal axis mitophagy mTORC1 muscle muscle atrophy muscle differentiation muscle diversification muscle homeostasis muscle pathology muscle phenotypes muscle populations muscle precursors muscle regeneration muscle satellite cell muscle stem cells muscles muscular dystrophy myofiber myofibril myofibroblasts myogenesis myogenic progenitors myostatin neonatal myosin neural cell adhesion molecule neuromuscular disorders neuromuscular junction NF-Y Nfix pericytes phagocytosis pharmacological approach Platelet-Rich Plasma proliferation radial growth regenerative medicine RhoA-ROCK1 sarcomere sarcopenia sarcoplasmic reticulum satellite cells septicemia single-cell skeletal muscle skeletal muscle growth skeletal muscle homeostasis skeletal muscle regeneration skeletal muscle stem and progenitor cells splicing isoforms splitting stem cell markers stem cells stem cells niche Tgfbr1 thyroid hormone tissue niche transdifferentiation transforming growth factor (TGF)-β1 transthyretin α-smooth muscle actin |
| Formato | Materiale a stampa |
| Livello bibliografico | Monografia |
| Lingua di pubblicazione | eng |
| Altri titoli varianti | Muscle Homeostasis and Regeneration |
| Record Nr. | UNINA-9910557587003321 |
Musarò Antonio
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| Basel, Switzerland, : MDPI - Multidisciplinary Digital Publishing Institute, 2020 | ||
| Lo trovi qui: Univ. Federico II | ||
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Stem Cell Research on Cardiology
| Stem Cell Research on Cardiology |
| Autore | David Robert |
| Pubbl/distr/stampa | Basel, Switzerland, : MDPI - Multidisciplinary Digital Publishing Institute, 2020 |
| Descrizione fisica | 1 online resource (356 p.) |
| Soggetto topico |
Biology, life sciences
Research and information: general |
| Soggetto non controllato |
18F-FDG PET
3D model 3D printing adult stem cells Akt signaling angiogenesis arrhythmia big conductance calcium activated potassium channel (BK) biomarker biomaterials bioprinting bioreactor biostable polyurethane bone marrow stem cells cardiac cellular regeneration cardiac differentiation cardiac function cardiac hypertrophy cardiac induced cells cardiac progenitor cells cardiac regeneration cardiac reprogramming cardiac tissue engineering cardiomyocyte proliferation cardiomyocytes cardioprotection cardiovascular disease cardiovascular diseases cardiovascular medicine coronary heart disease CRISPR/Cas9 genomic editing decorin direct reprogramming disease model drug/toxicity screening electrocardiography electrospinning endothelial progenitor cells endothelialization ESC Fabry disease fibronectin field potential genetic engineering heart heart valves human embryonic stem cells human induced pluripotent stem cell-derived cardiomyocytes (hiPSC-CMs) human pluripotent stem cell hypertrophic cardiomyopathy iberiotoxin induced pluripotent stem cells inflammation iPS cells iPSC KCa1.1 leukocytes long QT syndrome Mass spectrometry proteomic analysis maturation Maxi-K MEA mesenchymal stromal cells (MSC) meta-analysis micro-electrode-array MicroRNA microRNA (miR) Mir-133 miRNA mRNA multi-electrode-array myocardial infarction myocardial infraction myocarditis myocardium non-invasive imaging physical exercise PSC regeneration slo1 stem cells tissue engineering transdifferentiation vascular graft ventricular |
| Formato | Materiale a stampa |
| Livello bibliografico | Monografia |
| Lingua di pubblicazione | eng |
| Record Nr. | UNINA-9910557701803321 |
David Robert
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| Basel, Switzerland, : MDPI - Multidisciplinary Digital Publishing Institute, 2020 | ||
| Lo trovi qui: Univ. Federico II | ||
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The Retina in Health and Disease
| The Retina in Health and Disease |
| Autore | Ptito Maurice |
| Pubbl/distr/stampa | Basel, Switzerland, : MDPI - Multidisciplinary Digital Publishing Institute, 2021 |
| Descrizione fisica | 1 online resource (465 p.) |
| Soggetto topico |
Medicine and Nursing
Neurosciences |
| Soggetto non controllato |
3,5-DHBA
Ac2-26 African-American age-related macular degeneration AII amacrine cell altricial bird species Alzheimer's disease AMD amyloid angiogenesis angiography antioxidants apoptosis arterioles astrocytes ATP atypical cannabinoid receptors autophagy axon betulinic acid bioenergetics biomarker black catalase CD4+CD25+ cellular senescence Charles Bonnet syndrome clinical trials cognitive decline complement cascade complication development diabetes diabetes mellitus diabetic retinopathy dLGN Drp1 early detection eccentricity EEG electron microscopy electroretinography endoplasmic reticulum epidermal growth factor exendin-4 experimental models eye eye inflammation fingolimod FPR receptor functional analysis gap junction germ-free mice GFAP glucagon-like peptide-1 GPR81 growth cone GRP78 gut microbiome gut-retina axis HCAR1 HDAC high-fat diet histone deacetylase hyperglycemia hypoxia immunodeficient RCS rat immunohistochemistry inflammation inflammatory mediators iPSC iPSC-RPE ischemia-reperfusion injury kallikrein-kinin system kinin receptors lactate LED screen light damage lipopolysaccharide macroglia mesenchymal stem cells metabolism microglia microglia morphotype microvascular microvascular complications and dysfunction mitochondria monkeys motor protein Müller cells multiple sclerosis myosin 1C n/a natural bioactive extracts neurod neurodegeneration neuroprotection neurovascular unit Notch ON/OFF asymmetry optic nerve crush optic neuritis optical coherence tomography optical filter osteopontin outer segments oxidative stress parvalbumin photoreceptor photoreceptors precocial bird species progenitor cell programmed cell death Prox1 reactive oxygen species regeneration remodeling respiration resting state retina retinal degeneration retinal degenerative diseases retinal detachment retinal fluorescence imaging retinal ganglion cells retinal glial cell retinal inflammation retinal light injury retinal microglia retinal pigment epithelium retinal protection retinal transplantation retinal vessels retinogenesis retinopathy rhodopsin RNA sequencing senescence-associated galactosidase activity signal transducer and activator of transcription 3 spinal cord injury stem cell therapy stress response systemic disease trichostatin A (TSA) typical cannabinoid receptors ultrathin parylene unfolded protein response vascular endothelial growth factor (VEGF) vascularization visual function visual hallucination visual system zebrafish |
| Formato | Materiale a stampa |
| Livello bibliografico | Monografia |
| Lingua di pubblicazione | eng |
| Record Nr. | UNINA-9910557336603321 |
Ptito Maurice
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| Basel, Switzerland, : MDPI - Multidisciplinary Digital Publishing Institute, 2021 | ||
| Lo trovi qui: Univ. Federico II | ||
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Towards Mechanism-based Treatments for Fragile X Syndrome / Inbal Gazy, Daman Kumari
| Towards Mechanism-based Treatments for Fragile X Syndrome / Inbal Gazy, Daman Kumari |
| Autore | Gazy Inbal |
| Pubbl/distr/stampa | MDPI - Multidisciplinary Digital Publishing Institute, 2019 |
| Descrizione fisica | 1 electronic resource (250 p.) |
| Soggetto topico | Biology, life sciences |
| Soggetto non controllato |
lymphoblast
pluripotent stem cells FMR1 Gene editing X chromosome Fmr1 epigenetic gene silencing FMR1 gene Fragile X syndrome 1 repeat instability characteristics that have the greatest impact DNA instability working memory language development mosaicism CRISPR 3 clinical trials autism spectrum disorders Fmr1 KO mouse automated vocal analysis base excision repair (BER) inhibitory control cerebral spinal fluid iPSC drug development targeted treatments molecular biomarkers viral vector avoidance biomarker set-shifting early identification expansion anxiety planning voice of the person mismatch repair (MMR) gene reactivation double-strand break repair (DSBR) newborn screening intellectual disability processing speed voice of the patient fragile X syndrome adeno-associated virus neurodevelopmental disorders histone methylation Non-homologous end-joining (NHEJ) ASD Fxr2 Fragile X-associated Tremor/Ataxia Syndrome 2 Trinucleotide Repeat 4 CGG Repeat Expansion Disease DNA methylation contraction fragile X mental retardation protein RNA:DNA hybrid behavior developmental disorders cognition females FMRP Fragile X Syndrome unstable repeat diseases protein synthesis brain cognitive flexibility treatment development fibroblast PRC2 transcription coupled repair (TCR) best practices attention Fragile X executive function |
| ISBN |
9783039215065
303921506X |
| Formato | Materiale a stampa |
| Livello bibliografico | Monografia |
| Lingua di pubblicazione | eng |
| Record Nr. | UNINA-9910367759103321 |
Gazy Inbal
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| MDPI - Multidisciplinary Digital Publishing Institute, 2019 | ||
| Lo trovi qui: Univ. Federico II | ||
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