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Cellular and Molecular Mechanisms of Nephropathic Cystinosis
Cellular and Molecular Mechanisms of Nephropathic Cystinosis
Autore Levtchenko Elena N
Pubbl/distr/stampa Basel, : MDPI - Multidisciplinary Digital Publishing Institute, 2022
Descrizione fisica 1 electronic resource (230 p.)
Soggetto topico Medicine
Pharmacology
Soggetto non controllato cystinosis
cysteamine
bone
osteoclast
genotype
CD34+ hematopoietic stem and progenitor cells
gene therapy
pre-clinical studies
investigational new drug application
clinical trial
disulfiram
mice
zebrafish
fertility
azoospermia
hypogonadism
histopathology
mouse model
lysosomal storage disease
cell and animal models
infantile nephropathic cystinosis
bone-muscle wasting
fibroblast growth factor 23
osteoclasts
sclerostin
leptin
fractures
nephropathic cystinosis
hollow fiber membrane
3-dimensional models
autophagy
macrophages
inflammasome
proximal tubular cells
endocytosis
apoptosis
chitotriosidase
interleukins
galectin-3
novel therapies
endolysosome
epithelial cell differentiation
homeostasis
lysosomal storage diseases
mitochondrial distress
kidney proximal tubule
programmed cell death
central nervous system
cortical atrophy
arterial spin labelling
cystine blood level
lysosomal storage disorder
history
treatment strategies for cystinosis
newborn screening
clinical course
CTNS-pathogenic variants
newborn screening for cystinosis
kidney progenitors
cell model
biomarkers
cystine
kidney
therapeutic monitoring
Formato Materiale a stampa
Livello bibliografico Monografia
Lingua di pubblicazione eng
Record Nr. UNINA-9910585941103321
Levtchenko Elena N  
Basel, : MDPI - Multidisciplinary Digital Publishing Institute, 2022
Materiale a stampa
Lo trovi qui: Univ. Federico II
Opac: Controlla la disponibilità qui
Mixed Matrix Membranes
Mixed Matrix Membranes
Autore Casado-Coterillo Clara
Pubbl/distr/stampa MDPI - Multidisciplinary Digital Publishing Institute, 2019
Descrizione fisica 1 electronic resource (146 p.)
Soggetto non controllato modeling
neural tissue regeneration
membrane fabrication
nanoporous polybenzimidazole membranes
photo-assisted polymerization
poly (?-caprolactone)
supported ionic liquid membranes
CH4 selective membranes
flat-sheet membrane
hollow fiber membrane
ion exchange capacity
reduced graphene oxide
polymer of intrinsic microporosity
CH4 solubility
RHO
temperature
porous nanoparticles
protic imidazolium ionic liquids
POSS®
mixed matrix membranes
characterization techniques
membrane modification
in vitro human neural models
small-pore zeolites (CHA
Poly(trimethylsilyl-1-propyne) (PTMSP)
LTA)
filler dispersion
gas separation
water vapor
gas separation membrane
CO2 separation
nanocomposite membranes
hydrolytic bulk degradation mechanism
PVA
compatibility
borane
ISBN 3-03921-977-4
Formato Materiale a stampa
Livello bibliografico Monografia
Lingua di pubblicazione eng
Record Nr. UNINA-9910367737203321
Casado-Coterillo Clara  
MDPI - Multidisciplinary Digital Publishing Institute, 2019
Materiale a stampa
Lo trovi qui: Univ. Federico II
Opac: Controlla la disponibilità qui