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Cellular and Molecular Mechanisms of Nephropathic Cystinosis
Cellular and Molecular Mechanisms of Nephropathic Cystinosis
Autore Levtchenko Elena N
Pubbl/distr/stampa Basel, : MDPI - Multidisciplinary Digital Publishing Institute, 2022
Descrizione fisica 1 online resource (230 p.)
Soggetto topico Medicine and Nursing
Pharmacology
Soggetto non controllato 3-dimensional models
apoptosis
arterial spin labelling
autophagy
azoospermia
biomarkers
bone
bone-muscle wasting
CD34+ hematopoietic stem and progenitor cells
cell and animal models
cell model
central nervous system
chitotriosidase
clinical course
clinical trial
cortical atrophy
CTNS-pathogenic variants
cysteamine
cystine
cystine blood level
cystinosis
disulfiram
endocytosis
endolysosome
epithelial cell differentiation
fertility
fibroblast growth factor 23
fractures
galectin-3
gene therapy
genotype
histopathology
history
hollow fiber membrane
homeostasis
hypogonadism
infantile nephropathic cystinosis
inflammasome
interleukins
investigational new drug application
kidney
kidney progenitors
kidney proximal tubule
leptin
lysosomal storage disease
lysosomal storage diseases
lysosomal storage disorder
macrophages
mice
mitochondrial distress
mouse model
nephropathic cystinosis
newborn screening
newborn screening for cystinosis
novel therapies
osteoclast
osteoclasts
pre-clinical studies
programmed cell death
proximal tubular cells
sclerostin
therapeutic monitoring
treatment strategies for cystinosis
zebrafish
Formato Materiale a stampa
Livello bibliografico Monografia
Lingua di pubblicazione eng
Record Nr. UNINA-9910585941103321
Levtchenko Elena N  
Basel, : MDPI - Multidisciplinary Digital Publishing Institute, 2022
Materiale a stampa
Lo trovi qui: Univ. Federico II
Opac: Controlla la disponibilità qui
Mixed Matrix Membranes
Mixed Matrix Membranes
Autore Casado-Coterillo Clara
Pubbl/distr/stampa MDPI - Multidisciplinary Digital Publishing Institute, 2019
Descrizione fisica 1 online resource (146 p.)
Soggetto topico Technology: general issues
Soggetto non controllato borane
CH4 selective membranes
CH4 solubility
characterization techniques
CO2 separation
compatibility
filler dispersion
flat-sheet membrane
gas separation
gas separation membrane
hollow fiber membrane
hydrolytic bulk degradation mechanism
in vitro human neural models
ion exchange capacity
LTA)
membrane fabrication
membrane modification
mixed matrix membranes
modeling
nanocomposite membranes
nanoporous polybenzimidazole membranes
neural tissue regeneration
photo-assisted polymerization
poly (?-caprolactone)
Poly(trimethylsilyl-1-propyne) (PTMSP)
polymer of intrinsic microporosity
porous nanoparticles
POSS®
protic imidazolium ionic liquids
PVA
reduced graphene oxide
RHO
small-pore zeolites (CHA
supported ionic liquid membranes
temperature
water vapor
ISBN 3-03921-977-4
Formato Materiale a stampa
Livello bibliografico Monografia
Lingua di pubblicazione eng
Record Nr. UNINA-9910367737203321
Casado-Coterillo Clara  
MDPI - Multidisciplinary Digital Publishing Institute, 2019
Materiale a stampa
Lo trovi qui: Univ. Federico II
Opac: Controlla la disponibilità qui