Cellular and Molecular Mechanisms of Nephropathic Cystinosis |
Autore | Levtchenko Elena N |
Pubbl/distr/stampa | Basel, : MDPI - Multidisciplinary Digital Publishing Institute, 2022 |
Descrizione fisica | 1 electronic resource (230 p.) |
Soggetto topico |
Medicine
Pharmacology |
Soggetto non controllato |
cystinosis
cysteamine bone osteoclast genotype CD34+ hematopoietic stem and progenitor cells gene therapy pre-clinical studies investigational new drug application clinical trial disulfiram mice zebrafish fertility azoospermia hypogonadism histopathology mouse model lysosomal storage disease cell and animal models infantile nephropathic cystinosis bone-muscle wasting fibroblast growth factor 23 osteoclasts sclerostin leptin fractures nephropathic cystinosis hollow fiber membrane 3-dimensional models autophagy macrophages inflammasome proximal tubular cells endocytosis apoptosis chitotriosidase interleukins galectin-3 novel therapies endolysosome epithelial cell differentiation homeostasis lysosomal storage diseases mitochondrial distress kidney proximal tubule programmed cell death central nervous system cortical atrophy arterial spin labelling cystine blood level lysosomal storage disorder history treatment strategies for cystinosis newborn screening clinical course CTNS-pathogenic variants newborn screening for cystinosis kidney progenitors cell model biomarkers cystine kidney therapeutic monitoring |
Formato | Materiale a stampa ![]() |
Livello bibliografico | Monografia |
Lingua di pubblicazione | eng |
Record Nr. | UNINA-9910585941103321 |
Levtchenko Elena N
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Basel, : MDPI - Multidisciplinary Digital Publishing Institute, 2022 | ||
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Lo trovi qui: Univ. Federico II | ||
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Mixed Matrix Membranes |
Autore | Casado-Coterillo Clara |
Pubbl/distr/stampa | MDPI - Multidisciplinary Digital Publishing Institute, 2019 |
Descrizione fisica | 1 electronic resource (146 p.) |
Soggetto non controllato |
modeling
neural tissue regeneration membrane fabrication nanoporous polybenzimidazole membranes photo-assisted polymerization poly (?-caprolactone) supported ionic liquid membranes CH4 selective membranes flat-sheet membrane hollow fiber membrane ion exchange capacity reduced graphene oxide polymer of intrinsic microporosity CH4 solubility RHO temperature porous nanoparticles protic imidazolium ionic liquids POSS® mixed matrix membranes characterization techniques membrane modification in vitro human neural models small-pore zeolites (CHA Poly(trimethylsilyl-1-propyne) (PTMSP) LTA) filler dispersion gas separation water vapor gas separation membrane CO2 separation nanocomposite membranes hydrolytic bulk degradation mechanism PVA compatibility borane |
ISBN | 3-03921-977-4 |
Formato | Materiale a stampa ![]() |
Livello bibliografico | Monografia |
Lingua di pubblicazione | eng |
Record Nr. | UNINA-9910367737203321 |
Casado-Coterillo Clara
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MDPI - Multidisciplinary Digital Publishing Institute, 2019 | ||
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Lo trovi qui: Univ. Federico II | ||
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