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Cellular primary immunodeficiencies / / Mario Milco D'Elios, Cosima Tatiana Baldari, Francesco Annunziato, editors ; foreword by Donatella Lippi
Cellular primary immunodeficiencies / / Mario Milco D'Elios, Cosima Tatiana Baldari, Francesco Annunziato, editors ; foreword by Donatella Lippi
Edizione [1st ed. 2021.]
Pubbl/distr/stampa Cham, Switzerland : , : Springer, , [2021]
Descrizione fisica 1 online resource (XIV, 513 p. 41 illus., 38 illus. in color.)
Disciplina 616.0473
Collana Rare Diseases of the Immune System
Soggetto topico Immunodeficiency
Immune system - Cytopathology
Immunodeficiència
Patologia cel·lular
Sistema immunitari
Soggetto genere / forma Llibres electrònics
ISBN 3-030-70107-7
Formato Materiale a stampa
Livello bibliografico Monografia
Lingua di pubblicazione eng
Nota di contenuto 1. Primary Immunodeficiencies -- 2. Genetics of Cellular Immunodeficiencies -- 3. Phenocopies of Primary Immuno Deficiencies -- 4. Dysfunctional immune synapses in T cell immunodeficiencies -- 5. Mucosal immunity in primary immunodeficiencies -- 6. Combined Immuno Deficiencies -- 7. Congenital defects of phagocytes -- 8. Defects in intrinsic and innate immunity -- 9. Diseases of immune dysregulation -- 10. IPEX syndrome and IPEX-related disorders -- 11. Autoinflammatory disorders -- 12. Lung in Cellular Immunodeficiencies -- 13. Gut involvement in Cellular Immunodeficencies -- 14. Malignancies in Cellular Immunodeficencies -- 15. Autoimmunity in Cellular Immunodeficencies -- 16. Differential diagnostic in Cellular Immunodeficiencies -- 17. Management of Cellular Immunodeficiencies -- 18. Vaccines in Cellular Immunodeficiencies -- 19. Gene therapy in Cellular Immunodeficiencies.
Record Nr. UNINA-9910483482603321
Cham, Switzerland : , : Springer, , [2021]
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Encyclopedia of medical immunology : immunodeficiency diseases / / edited by Ian R. MacKay, 3 others
Encyclopedia of medical immunology : immunodeficiency diseases / / edited by Ian R. MacKay, 3 others
Edizione [1st ed. 2020.]
Pubbl/distr/stampa New York, New York : , : Springer, , [2020]
Descrizione fisica 1 online resource (73 illus., 60 illus. in color. eReference.)
Disciplina 354.81150006
Soggetto topico Immunologic diseases
Immunology
Immunodeficiency
ISBN 1-4614-8678-5
Formato Materiale a stampa
Livello bibliografico Monografia
Lingua di pubblicazione eng
Nota di contenuto From the Content: Complement Deficiencies -- Dysregulation -- Defects in Innate Immunity -- Combined Immunodeficiencies -- Combined Immunodeficiencies with Associated or Syndromic Features -- Predominantly Antibody deficiency -- Autoinflammatory Disorders -- Defects of Phagocyte Number, Function, or Both -- Evaluation and Management of Immunodeficiency.
Record Nr. UNINA-9910426055703321
New York, New York : , : Springer, , [2020]
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Neutropenia in Primary Immunodeficiency Diseases / / Neslihan Edeer Karaca
Neutropenia in Primary Immunodeficiency Diseases / / Neslihan Edeer Karaca
Autore Karaca Neslihan Edeer
Pubbl/distr/stampa London : , : IntechOpen, , 2021
Descrizione fisica 1 online resource (142 pages)
Disciplina 616.0473
Soggetto topico Immunodeficiency
ISBN 1-83969-078-X
Formato Materiale a stampa
Livello bibliografico Monografia
Lingua di pubblicazione eng
Nota di contenuto 1. Introduction -- 1.1 Primary genetic defects of severe congenital neutropenia -- 1.2 Disorders of molecular processing -- 1.2.1 Shwachmann-Diamond syndrome -- 1.2.2 Dyskeratosis congenita -- 1.3 Disorders of metabolism -- 1.3.1 Glycogen storage disease type Ib -- 1.3.2 Barth syndrome -- 1.3.3 Pearson syndrome -- 1.4 Vesicular trafficking disorders -- 1.4.1 Chediak-Higashi syndrome -- 1.4.2 Griscelli syndrome type 2 -- 1.4.3 Hermansky-Pudlac syndrome type 2 -- 1.4.4 P14 deficiency -- 1.4.5 Cohen syndrome -- 1.4.6 VPS45 deficiency -- 1.5 Well-known primary immunodeficiency diseases associated with neutropenia -- 1.5.1 Bruton's disease -- 1.5.2 CD40LG deficiency (Hyper IgM syndrome type I) -- 1.5.3 Severe combined immunodeficiency -- 1.5.4 Wiskott Aldrich syndrome -- 1.5.5 WHIM syndrome -- 1.5.6 Cartilage-hair hypoplasia -- 1.5.7 STK4/MST1 deficiency -- 1.5.8 GATA2 deficiency -- 2. Diagnostic work-up in chronic neutropenia -- 3. Treatment and follow-up -- 4. Conclusion -- References.
Altri titoli varianti Earth’s Crust and Its Evolution
Record Nr. UNINA-9910633983003321
Karaca Neslihan Edeer  
London : , : IntechOpen, , 2021
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Opportunistic intracellular bacteria and immunity [[electronic resource] /] / edited by Lois J. Paradise and Herman Friedman and Mauro Bendinelli
Opportunistic intracellular bacteria and immunity [[electronic resource] /] / edited by Lois J. Paradise and Herman Friedman and Mauro Bendinelli
Edizione [1st ed. 2002.]
Pubbl/distr/stampa New York, : Plenum Press, c1999
Descrizione fisica 1 online resource (329 p.)
Disciplina 616.9/2
Altri autori (Persone) ParadiseLois J
FriedmanHerman <1931-2007.>
BendinelliMauro
Collana Infectious agents and pathogenesis
Soggetto topico Bacterial diseases
Opportunistic infections
Immunodeficiency
Immunosuppression
Soggetto genere / forma Electronic books.
ISBN 0-585-42792-5
1-280-04275-3
9786610042753
0-306-46809-3
Formato Materiale a stampa
Livello bibliografico Monografia
Lingua di pubblicazione eng
Nota di contenuto Immune Defenses against Intracellular Bacterial Infections -- Genetic Regulation of Host Responses to Salmonella typhimurium -- Host Resistance and Mycobacterium tuberculosis Infection -- The Influence of Adrenal Steroids on Macrophage and T-cell Function in Tuberculosis -- Mycobacterium leprae as an Opportunistic Pathogen -- Immunology and Immunopathology of Mycobacterial Infections -- Mycobacterium avium-Complex Infections and Immunodeficiency -- Pathogenesis of Legionella pneumophila Infection -- Immune Responses to Legionella -- The Infectious/Pathogenic Processes Driven by Listeria monocytogenes in Laboratory Mice -- Rhodococcus equi: Pathogenesis and Replication in Macrophages -- Bartonella Infections in the Immunocompromised Host -- Chlamydia trachomatis Infections -- Chlamydia Infection and Pneumonia -- Brucella Infections and Immunity -- Antibiotic Treatment of Infections with Intracellular Bacteria.
Record Nr. UNINA-9910455001703321
New York, : Plenum Press, c1999
Materiale a stampa
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Opportunistic intracellular bacteria and immunity / / editors, Lois J. Paradise, Herman Friedman, Mauro Bendinelli
Opportunistic intracellular bacteria and immunity / / editors, Lois J. Paradise, Herman Friedman, Mauro Bendinelli
Edizione [First edition 2002.]
Pubbl/distr/stampa New York, : Plenum Press, c1999
Descrizione fisica 1 online resource (xxvi, 302 pages) : illustrations
Disciplina 616.9/2
Altri autori (Persone) ParadiseLois J
FriedmanHerman <1931-2007.>
BendinelliMauro
Collana Infectious agents and pathogenesis
Soggetto topico Bacterial diseases
Opportunistic infections
Immunodeficiency
Immunosuppression
ISBN 0-585-42792-5
1-280-04275-3
9786610042753
0-306-46809-3
Formato Materiale a stampa
Livello bibliografico Monografia
Lingua di pubblicazione eng
Nota di contenuto Immune Defenses against Intracellular Bacterial Infections -- Genetic Regulation of Host Responses to Salmonella typhimurium -- Host Resistance and Mycobacterium tuberculosis Infection -- The Influence of Adrenal Steroids on Macrophage and T-cell Function in Tuberculosis -- Mycobacterium leprae as an Opportunistic Pathogen -- Immunology and Immunopathology of Mycobacterial Infections -- Mycobacterium avium-Complex Infections and Immunodeficiency -- Pathogenesis of Legionella pneumophila Infection -- Immune Responses to Legionella -- The Infectious/Pathogenic Processes Driven by Listeria monocytogenes in Laboratory Mice -- Rhodococcus equi: Pathogenesis and Replication in Macrophages -- Bartonella Infections in the Immunocompromised Host -- Chlamydia trachomatis Infections -- Chlamydia Infection and Pneumonia -- Brucella Infections and Immunity -- Antibiotic Treatment of Infections with Intracellular Bacteria.
Record Nr. UNINA-9910779845703321
New York, : Plenum Press, c1999
Materiale a stampa
Lo trovi qui: Univ. Federico II
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Opportunistic intracellular bacteria and immunity / / editors, Lois J. Paradise, Herman Friedman, Mauro Bendinelli
Opportunistic intracellular bacteria and immunity / / editors, Lois J. Paradise, Herman Friedman, Mauro Bendinelli
Edizione [First edition 2002.]
Pubbl/distr/stampa New York, : Plenum Press, c1999
Descrizione fisica 1 online resource (xxvi, 302 pages) : illustrations
Disciplina 616.9/2
Altri autori (Persone) ParadiseLois J
FriedmanHerman <1931-2007.>
BendinelliMauro
Collana Infectious agents and pathogenesis
Soggetto topico Bacterial diseases
Opportunistic infections
Immunodeficiency
Immunosuppression
ISBN 0-585-42792-5
1-280-04275-3
9786610042753
0-306-46809-3
Formato Materiale a stampa
Livello bibliografico Monografia
Lingua di pubblicazione eng
Nota di contenuto Immune Defenses against Intracellular Bacterial Infections -- Genetic Regulation of Host Responses to Salmonella typhimurium -- Host Resistance and Mycobacterium tuberculosis Infection -- The Influence of Adrenal Steroids on Macrophage and T-cell Function in Tuberculosis -- Mycobacterium leprae as an Opportunistic Pathogen -- Immunology and Immunopathology of Mycobacterial Infections -- Mycobacterium avium-Complex Infections and Immunodeficiency -- Pathogenesis of Legionella pneumophila Infection -- Immune Responses to Legionella -- The Infectious/Pathogenic Processes Driven by Listeria monocytogenes in Laboratory Mice -- Rhodococcus equi: Pathogenesis and Replication in Macrophages -- Bartonella Infections in the Immunocompromised Host -- Chlamydia trachomatis Infections -- Chlamydia Infection and Pneumonia -- Brucella Infections and Immunity -- Antibiotic Treatment of Infections with Intracellular Bacteria.
Record Nr. UNINA-9910819209603321
New York, : Plenum Press, c1999
Materiale a stampa
Lo trovi qui: Univ. Federico II
Opac: Controlla la disponibilità qui