LEADER 04449oam 2200733I 450 001 9910456498103321 005 20200520144314.0 010 $a0-429-06998-7 010 $a1-282-56094-8 010 $a9786612560941 010 $a1-4398-0182-7 024 7 $a10.3109/9781439801826 035 $a(CKB)2550000000012095 035 $a(EBL)1407320 035 $a(SSID)ssj0000415378 035 $a(PQKBManifestationID)12155219 035 $a(PQKBTitleCode)TC0000415378 035 $a(PQKBWorkID)10410691 035 $a(PQKB)11244488 035 $a(MiAaPQ)EBC1407320 035 $a(MiAaPQ)EBC516896 035 $a(Au-PeEL)EBL1407320 035 $a(CaPaEBR)ebr10384020 035 $a(CaONFJC)MIL256094 035 $a(OCoLC)899155606 035 $a(OCoLC)613206351 035 $a(Au-PeEL)EBL516896 035 $a(EXLCZ)992550000000012095 100 $a20180331d2010 uy 0 101 0 $aeng 135 $aur|n|---||||| 181 $ctxt 182 $cc 183 $acr 200 00$aCystic fibrosis /$fedited by Julian L. Allen, Howard B. Panitch, and Ronald C. Rubenstein 210 1$aNew York, N.Y. :$cInforma Healthcare USA,$d2010. 215 $a1 online resource (546 p.) 225 1 $aLung biology in health and disease ;$v242 300 $aDescription based upon print version of record. 311 $a1-138-11261-5 311 $a1-4398-0181-9 320 $aIncludes bibliographical references and index. 327 $aFront Cover; Preface; Contents; Chapter 1. The Genetics of Cystic Fibrosis; Chapter 2. Ion Transport; Chapter 3. Mucus Abnormalities and Ciliary Dysfunction; Chapter 4. Microbiology in Cystic Fibrosis; Chapter 5. Inflammation in the Cystic Fibrosis Lung; Chapter 6. Modifier Genes of Cystic Fibrosis; Chapter 7. Cystic Fibrosis: Diagnosis, Sweat Testing, and Newborn Screening; Chapter 8. Diagnostic Approach to Diseases Associated with Cystic Fibrosis Transmembrane Conductance Regulator Gene Mutations; Chapter 9. Lung Function Testing in Infants 327 $aChapter 10. Assessment of Lung Function in Young Children with Cystic FibrosisChapter 11. Lung Function Testing in School-Age Children with Cystic Fibrosis; Chapter 12. Thoracic Imaging in Cystic Fibrosis Pulmonary Disease; Chapter 13. Pulmonary Manifestations; Chapter 14. Treatment Strategies for Maintaining Pulmonary Health in Cystic Fibrosis; Chapter 15. Mucolytic Therapy and Airway Clearance Techniques; Chapter 16. Pulmonary Exacerbations; Chapter 17. Gastrointestinal Complications of Cystic Fibrosis; Chapter 18. Liver Disease; Chapter 19. Nutrition; Chapter 20. Bone Health and Treatment 327 $aChapter 21. Cystic Fibrosis-Related Diabetes and ManagementChapter 22. Other extrapulmonary Complications and Treatment; Chapter 23. Chronic Respiratory Failure and the Roles of Noninvasive Ventilation and Lung Transplantation; Chapter 24. Gene Repair: Past, Present, and Future; Chapter 25. Restoration of CFTR Function with Small-Molecule Modulators; Chapter 26. Quality IMprovement in Cystic Fibrosis Care; Chapter 27. Cystic Fibrosis and Infection Control; Chapter 28. Transition to Adult Care; Chapter 29. Reproduction, Sexuality, and Fertility 327 $aChapter 30. A Biopsychosocial Model of Cystic Fibrosis: Social and Emotional Functioning, Adherence, and Quality of LifeChapter 31. Palliative and End-of-Life Care in Cystic Fibrosis; Index; Back Cover 330 $a

The median age of survival for those with cystic fibrosis has risen considerably in recent years. This text thoroughly examines the developments and breakthroughs which have led to this improvement in life expectancy. With a focus on the latest discoveries in the diagnosis and treatment of the disease, this book provides a comprehensive overview of the past, current and forthcoming advancements in cystic fibrosis research and clinical care.

410 0$aLung biology in health and disease ;$vv. 242. 606 $aCystic fibrosis 606 $aLungs$xDiseases 608 $aElectronic books. 615 0$aCystic fibrosis. 615 0$aLungs$xDiseases. 676 $a616.3/72 701 $aAllen$b Julian Lewis$01049589 701 $aRubenstein$b Ronald$01049590 701 $aPanitch$b Howard B$01049591 801 0$bMiAaPQ 801 1$bMiAaPQ 801 2$bMiAaPQ 906 $aBOOK 912 $a9910456498103321 996 $aCystic fibrosis$92478742 997 $aUNINA