LEADER 04973nam 22006015 450 001 9910300201803321 005 20200706150213.0 010 $a1-4471-2401-4 024 7 $a10.1007/978-1-4471-2401-6 035 $a(CKB)3710000000332147 035 $a(EBL)1964755 035 $a(OCoLC)900158263 035 $a(SSID)ssj0001424555 035 $a(PQKBManifestationID)11798395 035 $a(PQKBTitleCode)TC0001424555 035 $a(PQKBWorkID)11363953 035 $a(PQKB)10054191 035 $a(DE-He213)978-1-4471-2401-6 035 $a(MiAaPQ)EBC1964755 035 $a(PPN)183515676 035 $a(EXLCZ)993710000000332147 100 $a20150110d2015 u| 0 101 0 $aeng 135 $aur|n|---||||| 181 $ctxt 182 $cc 183 $acr 200 10$aOrphan Lung Diseases$b[electronic resource] $eA Clinical Guide to Rare Lung Disease /$fedited by Vincent Cottin, Jean-Francois Cordier, Luca Richeldi 205 $a1st ed. 2015. 210 1$aLondon :$cSpringer London :$cImprint: Springer,$d2015. 215 $a1 online resource (623 p.) 300 $aDescription based upon print version of record. 311 $a1-4471-2400-6 320 $aIncludes bibliographical references at the end of each chapters and index. 327 $a1. Orphan Lung Diseases: From definition to organisation of Care -- 2. The Challenge of clinical research in orphan lung diseases -- 3. Chronic bronchiolitis in adults -- 4. Diffuse bronchiectasis of genetic origin -- 5. Allergic bronchopulmonary mycosis -- 6. Orphan Tracheopathies -- 7. Amyloidosis and the respiratory tract -- 8. Churg-Strauss syndrome: A clinical and therapeutic approach -- 9. Granunomatosis with polyangiitis (Wegener?s granylomatosis) -- 10. Alveolar Hemorrhage -- 11. Pulmonary Involvement in Takayasu Arteritis and Behçet Disease -- 12. Pulmonary vascular manifestations of hereditary hemorrhagic -- 13. Hepatopulmonary syndrome -- 14. Non-Langerhans cell histiocytosis -including Erdheim-Chester disease- and the lung -- 15. Idiopathic eosinophilic pneumonia -- 16. Multiple cystic lung disease -- 17. Lymphangioleiomyomatosis -- 18. Pulmonary alveolar Proteinosis -- 19. Exogenous lipoid pneumonia -- 20. Pulmonary alveolar microlithiasis -- 21. Pulmonary Fibrosis and the many faces of UIP -- 22. The syndrome of combined pulmonary fibrosis and emphysema -- 23. Non-specific, Unclassifiable, and Rare Idiopathic Interstitial Pneumonia -- 24. Organizing Pneumonias -- 25. Interstitial lung disease in systemic sclerosis -- 26. Interstitial lung disease in connective tissue diseases other than systemic sclerosis -- 27. Interstitial Lung Disease in Undifferentiated Forms of Connective Tissue Disease -- 28. Langerhans cell Granulomatosis and smoking-related interstitial lung diseases -- 29. Rare causes and the spectrum of hypersensitivity penumonitis -- 30. Chronic beryllium disease and other insterstitial lung diseases of occupational origin -- 31. Lymphoproliferative lung disorders -- 32.  Pulmonary manifestations of hematological malignancies -- 33. Pulmonary hypertension in orphan lung diseases -- 34. Orphan and rare drug-induced and iatrogenic respiratory disease -- 35. From cancer mimicking orphan lung disease to orphan thoracic oncology -- 36. Rare Diffuse lung diseases of genetic origin. 330 $aFocusing on clinical practice, this book explores the less common diseases affecting the airways, systematic disorders with lung involvement, interstitial lung diseases and many other orphan conditions of the lungs. It helps the reader to diagnose and manage these rare orphan diseases. Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease  is a practical, informative book written by a team of international authors with much experience in rare pulmonary diseases.   Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease provides synthesized and easily accessible information about the main orphan lung diseases, to aid clinicians in charge of patients with rare disease, or who consider the diagnosis of a rare disease in their patient. 606 $aRespiratory organs?Diseases 606 $aInternal medicine 606 $aPneumology/Respiratory System$3https://scigraph.springernature.com/ontologies/product-market-codes/H33134 606 $aInternal Medicine$3https://scigraph.springernature.com/ontologies/product-market-codes/H33002 615 0$aRespiratory organs?Diseases. 615 0$aInternal medicine. 615 14$aPneumology/Respiratory System. 615 24$aInternal Medicine. 676 $a616 676 $a616.2 702 $aCottin$b Vincent$4edt$4http://id.loc.gov/vocabulary/relators/edt 702 $aCordier$b Jean-Francois$4edt$4http://id.loc.gov/vocabulary/relators/edt 702 $aRicheldi$b Luca$4edt$4http://id.loc.gov/vocabulary/relators/edt 906 $aBOOK 912 $a9910300201803321 996 $aOrphan Lung Diseases$91864473 997 $aUNINA