LEADER 03832nam 22005775 450 001 9910159389003321 005 20200703133529.0 010 $a3-319-41349-X 024 7 $a10.1007/978-3-319-41349-5 035 $a(CKB)3710000001019171 035 $a(DE-He213)978-3-319-41349-5 035 $a(MiAaPQ)EBC4784148 035 $a(PPN)198341393 035 $a(EXLCZ)993710000001019171 100 $a20170109d2017 u| 0 101 0 $aeng 135 $aurnn|008mamaa 181 $ctxt$2rdacontent 182 $cc$2rdamedia 183 $acr$2rdacarrier 200 10$aSystemic Fibroinflammatory Disorders /$fedited by Augusto Vaglio 205 $a1st ed. 2017. 210 1$aCham :$cSpringer International Publishing :$cImprint: Springer,$d2017. 215 $a1 online resource (XII, 243 p. 33 illus., 22 illus. in color.) 225 1 $aRare Diseases of the Immune System,$x2282-6505 311 $a3-319-41347-3 320 $aIncludes bibliographical references and index. 327 $aPreface -- 1 Genetics of fibro-inflammatory disorders -- 2 Basic mechanisms linking inflammation and fibrosis -- 3 Histopathology of systemic fibro-inflammatory disorders -- 4 IgG4-related disorders: clinical and therapeutic aspects -- 5 IgG4-related disorders: pathophysiology -- 6 IgG4-related nephropathy -- 7 Autoimmune (IgG4-related) pancreatitis and sclerosing cholangitis -- 8 Sclerosing forms of autoimmune thyroiditis: from Hashimoto?s to Riedel?s to IgG4-related forms -- 9 Chronic periaortitis/retroperitoneal fibrosis: overview -- 10 Diffuse periaortitis -- 11 Treatment of chronic periaortitis/retroperitoneal fibrosis -- 12 Mediastinal fibrosis -- 13 Erdheim-Chester disease -- 14 Nephrogenic systemic fibrosis -- 15 Sclerosing mesenteritis -- 16 Malignant diseases mimicking retroperitoneal fibrosing disorders -- Subject Index. 330 $aThis book provides detailed information on the nosology, pathology, pathogenesis, clinical presentation, diagnosis and treatment of fibro-inflammatory disorders, rare diseases that often display systemic organ involvement. Among the conditions considered are IgG4-related disease, sclerosing cholangitis, Hashimoto?s and Riedel?s thyroiditis, retroperitoneal fibrosis/chronic periaortitis, mediastinal fibrosis, Erdheim-Chester disease, gadolinium-induced fibrosis, and sclerosing mesenteritis. This group of entities is still poorly defined and is characterized by the common denominator of chronic inflammatory infiltrate admixed with abundant fibrosis. IgG4-related disease is the prototypical example. Systemic Fibroinflammatory Disorders is the first book to draw together information on these conditions. As these diseases often require an interdisciplinary approach, the book is addressed to specialists of different disciplines, especially internists, rheumatologists, nephrologists, clinical immunologists, and hematologists. 410 0$aRare Diseases of the Immune System,$x2282-6505 606 $aRheumatology 606 $aImmunology 606 $aNephrology 606 $aRheumatology$3https://scigraph.springernature.com/ontologies/product-market-codes/H33170 606 $aImmunology$3https://scigraph.springernature.com/ontologies/product-market-codes/B14000 606 $aNephrology$3https://scigraph.springernature.com/ontologies/product-market-codes/H33126 615 0$aRheumatology. 615 0$aImmunology. 615 0$aNephrology. 615 14$aRheumatology. 615 24$aImmunology. 615 24$aNephrology. 676 $a616.72305 702 $aVaglio$b Augusto$4edt$4http://id.loc.gov/vocabulary/relators/edt 801 0$bMiAaPQ 801 1$bMiAaPQ 801 2$bMiAaPQ 906 $aBOOK 912 $a9910159389003321 996 $aSystemic Fibroinflammatory Disorders$91758835 997 $aUNINA