LEADER 01614nam0-2200397---450- 001 990008863500403321 005 20100125162349.0 010 $a960-7099-04-4 035 $a000886350 035 $aFED01000886350 035 $a(Aleph)000886350FED01 035 $a000886350 100 $a20090608d1990----km-y0itay50------ba 101 2 $alat$agrc$agre 102 $aGR 105 $ay-------001yy 200 1 $aBoethius, De topicis differentiis kai oi byzantines metaphraseis ton Manouel Holobolou kai Prochorou Kydone$feisagoge kai kritike ekdose ton keimenon ypo Demetriou Z. Niketa$gparartema/Anhang: eine Pachymeres-Weiterbearbeitung der Holobolos-Übersetzung 210 $aAthenai$cAkademia Athenon$aParis$cVrin$aBruxelles$cOusia$d1990 215 $aCLIV, 270 p.$d24 cm 225 1 $aCorpus philosophorum Medii Aevi$iPhilosophi byzantini$d=Byzantinoi philosophoi$v5 307 $aCopertina rigida 310 $aRil. in tela 500 10$aDe differentiis topicis$m$929505 517 1 $aBoethius, De topicis differentiis und die byzantinische Rezeption dieses Werkes 610 0 $aBoezio$aDe differentiis topicis$aTraduzioni e rielaborazioni$aEtà bizantina 676 $a189 700 1$aBoethius,$bAnicius Manlius Torquatus Severinus$f<475/480-ca. 524/525>$0182801 702 1$aPachymeres,$bGeorgius 702 1$aNikitas,$bDimitrios Z. 801 0$aIT$bUNINA$gRICA$2UNIMARC 901 $aBK 912 $a990008863500403321 952 $aP2B-650-BOETHIUS-402A-1990$bBibl. 27354$fFLFBC 959 $aFLFBC 996 $aDe differentiis topicis$929505 997 $aUNINA LEADER 06026nam 22008415 450 001 9910300341103321 005 20251117080044.0 010 $a3-662-44587-5 024 7 $a10.1007/978-3-662-44587-7 035 $a(CKB)3710000000277576 035 $a(EBL)1968518 035 $a(SSID)ssj0001386567 035 $a(PQKBManifestationID)11814661 035 $a(PQKBTitleCode)TC0001386567 035 $a(PQKBWorkID)11374162 035 $a(PQKB)11003656 035 $a(MiAaPQ)EBC1968518 035 $a(DE-He213)978-3-662-44587-7 035 $a(PPN)183091388 035 $a(EXLCZ)993710000000277576 100 $a20141105d2014 u| 0 101 0 $aeng 135 $aur|n|---||||| 181 $ctxt 182 $cc 183 $acr 200 10$aJIMD Reports Volume 16 /$fedited by Johannes Zschocke, K. Michael Gibson, Garry Brown, Eva Morava, Verena Peters 205 $a1st ed. 2014. 210 1$aBerlin, Heidelberg :$cSpringer Berlin Heidelberg :$cImprint: Springer,$d2014. 215 $a1 online resource (113 p.) 225 1 $aJIMD Reports,$x2192-8304 ;$v16 300 $aDescription based upon print version of record. 311 08$a3-662-44586-7 320 $aIncludes bibliographical references. 327 $aContents; Leucine Loading Test is Only Discriminative for 3-Methylglutaconic Aciduria Due to AUH Defect; Abstract; Introduction; Material and Methods; Patients; Leucine Loading Tests; Urinary Organic Acid Analysis; Leucine Loading Tests in Patients Described in the Literature; Results; Discussion; Disclosures; Compliance with Ethics Guidelines; Conflict of Interest; Informed Consent; Details of the Contributions of Individual Authors; References; Fabry Disease: Multidisciplinary Evaluation After 10 Years of Treatment with Agalsidase Beta; Abstract; Introduction; Objective 327 $aMaterials and MethodsStatistical Analysis; Results; Discussion; Conclusions; Take-Home Message; Compliance with Ethics Guidelines; Conflict of Interest; Informed Consent; Details of the Contributions of Individual Authors; References; Chondroitin 6-Sulfate as a Novel Biomarker for Mucopolysaccharidosis IVA and VII; Abstract; Introduction; Materials and Method; Subjects; Chemicals and Materials; Sample Preparation; Apparatus; Method Validation; Statistical Analysis; Results; LC-MS/MS Conditions; Calibration Curves; Precision and Accuracy; Chondroitin 6-Sulfate (C6S) Levels 327 $aKeratan Sulfate (KS) LevelCorrelation Between KS and C6S Levels; Discussion; Compliance with Ethics Guidelines; Conflict of Interest; Informed Consent; Animal Rights; Contributions to the Project; References; Carnitine Profile and Effect of Suppletion in Children with Renal Fanconi Syndrome due to Cystinosis; Abstract; Background; Patients and Methods; Results; Discussion; Synopsis; Compliance with Ethics Guidelines; Conflict of Interest; Informed Consent; Details of the Contributions of Individual Authors; References 327 $aCognitive and Antipsychotic Medication Use in Monoallelic GBA-Related Parkinson DiseaseAbstract; Introduction; Methods; Data Collection; Statistical Analysis; Results; Discussion; Sources of Support; Synopsis Sentence; Compliance with Ethics Guidelines; Conflict of Interest; Other Disclosures; Informed Consent; Animal Rights; Individual Author Contributions; Guarantor; References; Laronidase Replacement Therapy and Left Ventricular Function in Mucopolysaccharidosis I; Abstract; Introduction; Case Report; Methods; Conventional, Pulse Doppler, and Speckle Tracking Echocardiograms 327 $aStatistical AnalysisResults; Clinical Findings After LRT; Echocardiographic Findings After LRT; Relation of LV Weight to Urinary Uronic Acid Concentration, Diastolic Function, and Contraction Synchrony; Discussion; Limitations; Funding; Disclosure; Synopsis; Compliance with Ethics Guidelines; Conflict of Interest; Informed Consent; Animal Rights; Author Contributions; Competing Interests; Funding; References; Fibrolamellar Hepatocellular Carcinoma Mimicking Ornithine Transcarbamylase Deficiency; Abstract; Introduction; Case Report; Discussion; Synopsis 327 $aDetails of the Contributions of Individual Authors 330 $aJIMD Reports publishes case and short research reports in the area of inherited metabolic disorders. 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