01446nam 2200397 n 450 99639092880331620221108022457.0(CKB)1000000000664367(EEBO)2240868270(UnM)99840006(EXLCZ)99100000000066436719910125d1595 uy |engurbn||||a|bb|An apologie of infants[electronic resource] in a sermon: prouing, by the reuealed will of God, that children preuented by death of their baptisme, by Gods election, may be saued. By W.H. preacher in the Tower of London. Seene and allowed by authoritieAt London Printed by the widowe Orwin for Thomas Man1595[16], 61, [3] pDedication signed: William Hubbocke.The last leaf is blank.Running title reads: A sermon touching the vnbaptized.Reproduction of the original in the Peterborough Cathedral. Library.eebo-0124Infant salvationEarly works to 1800Sermons, English16th centuryInfant salvationSermons, EnglishHubbock Williamb. 1560.1013593Cu-RivESCu-RivESUk-ESCStRLINWaOLNBOOK996390928803316An apologie of infants2366789UNISA04163nam 22006615 450 991091859480332120241220115626.09783031708350303170835010.1007/978-3-031-70835-0(MiAaPQ)EBC31855060(Au-PeEL)EBL31855060(CKB)37058976900041(DE-He213)978-3-031-70835-0(OCoLC)1482267341(EXLCZ)993705897690004120241220d2024 u| 0engurcnu||||||||txtrdacontentcrdamediacrrdacarrierThe Extracellular Matrix in Genetic Skeletal Disorders /edited by Antonio Rossi, Frank Zaucke1st ed. 2024.Cham :Springer Nature Switzerland :Imprint: Springer,2024.1 online resource (414 pages)Biology of Extracellular Matrix,2191-1959 ;169783031708343 3031708342 Part I: ECM proteins and skeletal disorders -- Chapter 1: Extracellular matrix and skeletal dysplasias -- Chapter 2: Osteogenesis imperfecta and related diseases – collagen I alterations in skeletal and extraskeletal tissues -- Chapter 3: Bone involvement in the Ehlers-Danlos syndromes -- Chapter 4: Collagen II mutations in inherited cartilage diseases: our current understanding of genotype-phenotype correlations -- Chapter 5: Skeletal disorders linked to GAG synthesis -- Chapter 6: GAG sulfation and skeletal disorders -- Chapter 7: The fibrillinopathies – fibrillin-dependent skeletal dysplasias affecting long bone growth -- Part II: ECM signaling and skeletal disorders -- Chapter 8: FGF signaling: a key pathway during skeletal development -- Chapter 9: Impaired Wnt signaling as a cause of skeletal disorders -- Chapter 10: The skeletal ciliopathies -- Part III: Intracellular trafficking of ECM proteins and related skeletal disorders -- Chapter 11: Microtubule-associated motor proteins in skeletal development and health -- Chapter 12: COG4 variant and Saul-Wilson Syndrome -- 13: Membrane trafficking to the extracellular matrix and skeletal dysplasia.This book explores how defects in extracellular matrix (ECM) proteins, their post-translational modifications, and intracellular trafficking impact cartilage and bone integrity. It underscores the ECM's role in providing structural support, establishing morphogenetic gradients, and interacting with cell surface receptors in musculoskeletal tissues. The book delves into the structure and biology of the ECM in the skeleton, discussing skeletal disorders caused by mutations in genes associated with ECM proteins, synthesis, turnover, and signal transduction. Authored by experts who have made significant discoveries in the molecular mechanisms of skeletal disorders and are developing therapeutic strategies, this book is an invaluable research for both scientists and clinicians seeking a comprehensive understanding of this growing and exciting field. The series Biology of Extracellular Matrix is published in collaboration with the American Society for Matrix Biology and the International Society for Matrix Biology.Biology of Extracellular Matrix,2191-1959 ;16CytologyMusculoskeletal systemClinical biochemistryDiseasesCell BiologyMusculoskeletal systemMedical BiochemistryMechanisms of DiseaseCytology.Musculoskeletal system.Clinical biochemistry.Diseases.Cell Biology.Musculoskeletal system.Medical Biochemistry.Mechanisms of Disease.571.6Rossi Antonio336364Zaucke Frank1780939MiAaPQMiAaPQMiAaPQBOOK9910918594803321The Extracellular Matrix in Genetic Skeletal Disorders4305526UNINA04422nam 22007335 450 991102197010332120250824130202.09783031967788(electronic bk.)978303196777110.1007/978-3-031-96778-8(MiAaPQ)EBC32270646(Au-PeEL)EBL32270646(CKB)40410733000041(DE-He213)978-3-031-96778-8(EXLCZ)994041073300004120250824d2025 u| 0engurcnu||||||||txtrdacontentcrdamediacrrdacarrierVoices of Gen Z Shaping Transitions in the City of Peace and Justice /by Rosa Groen, Tahir Abbas1st ed. 2025.Cham :Springer Nature Switzerland :Imprint: Palgrave Macmillan,2025.1 online resource (151 pages)Palgrave Advances in Child Justice,3091-4280Print version: Groen, Rosa Voices of Gen Z Cham : Palgrave Macmillan,c2025 9783031967771 1 Introduction -- 2 Theory -- 3 Study 2022: Young people in Schilderswijk, Laakkwartier, and Moerwijk -- 4 Study 2023: Conflicting Perceptions of SDG16 and EU Climate Policies -- 5 Study 2024: Bringing the Groups Together: Youth groups in dialogue with policymakers -- 6 Discussion and Conclusions.This book provides empirical evidence on youth engagement with peace, justice, and strong institutions (SDG 16). It takes a bottom-up approach to exploring the meaning and value of global citizenship and social cohesion. It showcases three studies about how the younger generation interprets SDG 16, EU Climate policies (such as the European Green Deal) and the goals of The Hague as the International City of Peace and Justice. The city of The Hague is dedicated to the promotion of peace, justice, inclusivity and security and yet it is one of the most segregated cities in the Netherlands. This book challenges the assumptions that young people are uninterested in local decision-making or lack the competence to contribute to improving their neighborhoods. It gives voice to young people, generation Z (13-25 years old), in disadvantaged and advantaged areas in The Hague examining the experiences they have, their views in contrast with those of educators and policymakers in The Hague, and their views compared to different areas and age groups in The Hague. This book brings together multiple funded projects to discuss how we can engage young people in democratic processes including policymaking and societal challenges. It helps to bridge the gap between young people and policymakers and therefore speaks to policymakers, academics, students and lecturers on social cohesion, criminology, and social policies. Rosa Groen was most recently interim Professor of Global Citizenship at TheHague University of Applied Sciences (THUAS) and a visiting scholar at Leiden University, the Netherlands, in 2024. Tahir Abbas is Professor of Radicalisation Studies at the Institute of Security and Global Affairs at Leiden University in The Hague, the Netherlands. .Palgrave Advances in Child Justice,3091-4280Family policyJuvenile delinquentsPolitical sociologyCitizenshipStudy and teachingCriminologyPeaceChildren, Youth and Family PolicyYouth Offending and Juvenile JusticePolitical SociologyCitizenship EducationCrime Control and SecurityPeace and Conflict StudiesFamily policy.Juvenile delinquents.Political sociology.CitizenshipStudy and teaching.Criminology.Peace.Children, Youth and Family Policy.Youth Offending and Juvenile Justice.Political Sociology.Citizenship Education.Crime Control and Security.Peace and Conflict Studies.361.61362Groen Rosa1826738Abbas Tahir707053MiAaPQMiAaPQMiAaPQ9911021970103321Voices of Gen Z4429173UNINA