01161nam2 22002773i 450 VAN006763320240319030432.269978-88-432-0061-020090304d2008 |0itac50 baengUS|||| |||||ˆ3: ‰Dynamic behaviour, stability and emergency controlsRoberto Marconato2. edMilanoCEI2008XXXI, 910 p.ill.25 cm001VAN00676292001 Electric power systemsRoberto Marconato210 MilanoCEI215 volumi25 cm300 Trad. di Stefania Saraceni.3MilanoVANL000284MarconatoRobertoVANV0536593969Comitato elettrotecnico italiano <editore>VANV111517650ITSOL20240322RICABIBLIOTECA DEL DIPARTIMENTO DI INGEGNERIAIT-CE0100VAN05VAN0067633BIBLIOTECA DEL DIPARTIMENTO DI INGEGNERIA05PREST K 441 05VS 5167 20090304 BuonoDynamic behaviour, stability and emergency controls1437172UNICAMPANIA02352nim 2200493Ka 450 991014886610332120240912110819.00-00-759570-0(CKB)3710000000924090(BIP)049328789(ODN)ODN0002102773(EXLCZ)99371000000092409020161226d2015 uy 0enguruna---|||||spwrdacontentsrdamediacrdamediacrrdacarrierThe girl with seven names A north korean defector's story. /Hyeonseo LeeUnabridged.Glasgow William Collins20151 online resource (9 audio files) digitalUnabridged.NEW YORK TIMES BESTSELLER An extraordinary insight into life under one of the world's most ruthless and secretive dictatorships – and the story of one woman's terrifying struggle to avoid capture/repatriation and guide her family to freedom. As a child growing up in North Korea, Hyeonseo Lee was one of millions trapped by a secretive and brutal communist regime. Her home on the border with China gave her some exposure to the world beyond the confines of the Hermit Kingdom and, as the famine of the 1990s struck, she began to wonder, question and to realise that she had been brainwashed her entire life. Given the repression, poverty and starvation she witnessed surely her country could not be, as she had been told "the best on the planet"? Aged seventeen, she decided to escape North Korea. She could not have imagined that it would be twelve years before she was reunited with her family.Girl with Seven Names, TheNonfictionOverDriveBiography & AutobiographyOverDrivePoliticsOverDriveBiography & autobiographyPolitical scienceBiographyNonfiction.Biography & Autobiography.Politics.951.93043092BIO022000BIO026000POL035000POL042030bisacshLee Hyeonseo1774933John DavidothDunn JosieothAUDIO9910148866103321The girl with seven names4288463UNINA05759nam 2201441z- 450 991055757800332120220111(CKB)5400000000043869(oapen)https://directory.doabooks.org/handle/20.500.12854/76272(oapen)doab76272(EXLCZ)99540000000004386920202201d2021 |y 0engurmn|---annantxtrdacontentcrdamediacrrdacarrierHereditary Hemorrhagic TelangiectasiaRecent Advances and Future ChallengesBasel, SwitzerlandMDPI - Multidisciplinary Digital Publishing Institute20211 online resource (228 p.)3-0365-0590-3 3-0365-0591-1 Hereditary hemorrhagic telangiectasia (HHT) is an inherited disease that affects the blood vessels, and is characterized by direct connections between arteries and veins with no intervening capillaries. These abnormal vessels may appear in the skin as tiny red dilated blood vessels in the mouth, lips, fingers and toes. The presence of these vascular lesions in the mucosa can lead to spontaneous and recurrent nose bleeding, typically beginning in mid-childhood, and this is the most common clinical manifestation of HHT, occurring in over 90% of patients. Gastrointestinal bleeding, derived from mucocutaneous vascular lesions, affects approximately 25% of patients, almost always presenting after the age of 50. Chronic nasal and gastrointestinal bleeding can cause iron-deficiency anemia, and current therapeutic strategies are trying to minimize iron and blood transfusions. HHT patients also present large vascular lesions, known as arteriovenous malformations, that occur in internal organs like lungs, liver, and brain, and may result in life-threatening complications often related to the shunting of blood. This book not only highlights the current knowledge regarding diagnosis and treatment of HHT, but also the newest insights in the molecular basis of HHT, the understanding of which is essential for the development of new medicines or therapeutic strategies.Hereditary Hemorrhagic Telangiectasia Research and information: generalbicsscactivin receptor-like kinase 1 (ALK1)activin-receptor-like kinase 1ACVRL1ALK1angiogenesisantiangiogenic propertiesanticoagulantsantiplateletsantithrombotic therapyarteriovenous malformationarteriovenous malformation (AVM)arteriovenous malformations (AVMs)AVMbazedoxifenebevacizumabbiomarkerbiomarkersbleedingbone morphogenetic protein (BMP)catheter based embolization therapycell adhesioncerebral ischemic lesionscontrast enhanced magnetic resonance angiographyendoglinEndoglinendothelial cellsENGepistaxisepistaxis severity scoreetamsylateFK506gastrointestinal bleedinggenetic diseasegenotype-phenotype correlationguidelineshereditary hemorrhagichereditary hemorrhagic telangiectasiaHereditary hemorrhagic telangiectasiaHereditary Hemorrhagic Telangiectasiahereditary hemorrhagic telangiectasia (HHT)hereditary hemorrhagic telangiectasia (HHT), second-hithereditary hemorrhagic telangiectasia/HHT/osler's diseaseHHTinflammationlife expectancyliverlong non-coding RNAsmechanical damagemicroRNAmicroRNAsMRIN-acetylcysteinenasal endoscopynasal ointmentnon-coding RNAsnosebleedsOsler-Weber-Rendupediatricsplasmapropranololpropranolol gelpulmonary arteriovenous malformationpulmonary arteriovenous malformationsraloxifenerare diseaserare diseasessafetyscreeningshear stressSmad pathwaySmad4SMAD4somatic mutationsun-induced traumasurvivaltacrolimustelangiectasestelangiectasiatelangiectasistranexamic acidtranscatheter embolotherapytransforming growth factor beta (TGF-β)transforming growth factor-beta (TGF-β)ultrasoundvascular endothelial growth factor (VEGF)vascular injuryvascular malformationsResearch and information: generalMager Hans-Jurgenedt1299262Bernabeu CarmeloedtPost MarcoedtMager Hans-JurgenothBernabeu CarmeloothPost MarcoothBOOK9910557578003321Hereditary Hemorrhagic Telangiectasia3025091UNINA