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1. |
Record Nr. |
UNISA996395092203316 |
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Titolo |
By the King. A proclamation for the calling in all moneys of gold and silver coyned or stamped with the cross and harp, and the circumscription, the Commonwealth of England; and for making the same to be current onely to the first of December next, and no longer [[electronic resource]] |
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Pubbl/distr/stampa |
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London, : Printed by John Bill and Christopher Barker, printers to the King's most excellent Majesty, 1661. At the King's printing-house in Black-Fryars |
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Descrizione fisica |
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Altri autori (Persone) |
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Charles, King of England, <1630-1685.> |
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Soggetti |
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Coinage - Law and legislation - England |
Money - England |
Monetary policy - England |
Great Britain History Charles II, 1660-1685 Early works to 1800 |
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Lingua di pubblicazione |
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Formato |
Materiale a stampa |
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Livello bibliografico |
Monografia |
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Note generali |
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At end of text: Given at our court at Whitehal, the seventh day of September, 1661. in the thirteenth year of our raign. |
Steele notation: of of 2) unwil- there; Arms 67. |
Reproduction of originals in the British Library. |
Three copies of this item are filmed consecutively at reel C18:1[118]-[120]. |
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Sommario/riassunto |
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2. |
Record Nr. |
UNINA9910787948803321 |
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Titolo |
Inborn errors of metabolism : from neonatal screening to metabolic pathways / / edited by Brendan H. Lee and Fernando Scaglia |
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Pubbl/distr/stampa |
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Oxford, [England] ; ; New York, New York : , : Oxford University Press, , 2015 |
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©2015 |
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ISBN |
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0-19-939850-X |
0-19-979768-4 |
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Descrizione fisica |
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1 online resource (393 p.) |
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Collana |
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Oxford Monographs on Medical Genetics |
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Disciplina |
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Soggetti |
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Metabolism, Inborn errors of |
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Lingua di pubblicazione |
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Formato |
Materiale a stampa |
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Livello bibliografico |
Monografia |
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Note generali |
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Description based upon print version of record. |
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Nota di bibliografia |
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Includes bibliographical references and index. |
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Nota di contenuto |
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Cover; Series; Inborn Errors of Metabolism; Copyright; Contents; Contributors; About the Editors; Introduction; Section 1 Newborn Screening; 1 Newborn Screening for Inborn Errors of Metabolism: Introduction and Approaches for Confirmation; Section 2 Pathways; 2 Human Glycosylation Disorders: Many Faces, Many Pathways; 3 Gluconeogenesis; 4 Branched Chain Amino Acid Disorders; 5 Glycolysis; 6 Urea Cycle: Ureagenesis and Non-Ureagenic Functions; 7 Fatty Acid Metabolism and Defects; 8 Mitochondrial Disorders; 9 Cholesterol, Sterols, and Isoprenoids; 10 Disorders of One-Carbon Metabolism |
11 Neurotransmission and Neurotoxicity (Phenylketonuria and Dopamine)Section 3 Therapeutic Approaches; 12 Cell and Organ Transplantation for Inborn Errors of Metabolism; 13 Gene Replacement Therapy for Inborn Errors of Metabolism; 14 Enzyme Replacement and Other Therapies for the Lysosomal Storage Disorders; 15 Chaperone Therapy for the Lysosomal Storage Disorders; 16 Substrate Deprivation Therapy; Index; Colour Plate |
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Sommario/riassunto |
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Texts on inborn errors of metabolism (IEMs) have traditionally focused on classical biochemistry, clinical presentation, and standard treatment approaches. Inborn Errors of Metabolism is an expansion on this model, one that establishes an innovative pathway approach and provides a new authority on this family of disease. Alongside the |
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standard cadre of molecular and clinical underpinnings, this volume includes coverage of newborn screenings and an overarching treatment of IEMs as complex diseases -- how basic alterations can lead to complex secondary and tertiary effects in metabolism that con |
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