1.

Record Nr.

UNINA9910337509603321

Titolo

Auto-Inflammatory Syndromes [[electronic resource] ] : Pathophysiology, Diagnosis, and Management / / edited by Petros Efthimiou

Pubbl/distr/stampa

Cham : , : Springer International Publishing : , : Imprint : Springer, , 2019

ISBN

3-319-96929-3

Edizione

[1st ed. 2019.]

Descrizione fisica

1 online resource (XIX, 322 p. 39 illus., 31 illus. in color.)

Disciplina

616.723

Soggetti

Rheumatology

Immunology

Lingua di pubblicazione

Inglese

Formato

Materiale a stampa

Livello bibliografico

Monografia

Nota di contenuto

Introduction -- SECTION I: Pediatric Auto-Inflammatory Syndromes -- Systemic Arthritis -- Hyper-IgD -- TRAPS -- Schnitzler’s Syndrome -- Papa Syndrome -- Blau Syndrome -- Dira Syndrome -- Cryopyrin Associated Periodic Syndromes -- Transition of Care: When the Pediatric Patient Becomes an Adult -- SECTION II: Adult Auto-Inflammatory Syndromes -- Adult Onset Still’s Disease -- Idiopathic Recurrent Pericarditis -- Familial Mediterranean Fever -- Behcet’s Disease -- Interferonopathies -- Sweet’s Syndrome -- Anti-synthetase Syndrome -- Crystal Arthropathies -- Urticarial Vasculitis -- Relapsing Polychondritis.

Sommario/riassunto

This book provides an overview of auto-inflammatory syndromes, covering the underlying immune mechanisms that lead to their development, specific disease presentations, and clinical treatment guidelines. The book is divided into two sections, adult and pediatric, with chapters focusing on individuals diseases such as systemic arthritis, hyper-IgD, pap syndrome, idiopathic recurrent pericarditis, and familial Mediterranean fever. Chapters incorporate the most recent advances in disease pathophysiology and examine the underlying inductive and effector mechanisms and therapies that relate to each auto-inflammatory disorder at the genetic, molecular, cellular, and epidemiologic levels. The book also discusses the research behind



auto-inflammatory disorders to offer detailed clinical guidelines regarding diagnostic techniques, treatment plans, and advice on how to best transition pediatric patients into adult treatment. This is an invaluable reference on auto-inflammatory syndromes for clinicians and researchers in pediatric and adult rheumatology and immunology.