1.

Record Nr.

UNINA9910300332403321

Titolo

Behçet's Syndrome : From Pathogenesis to Treatment / / edited by Lorenzo Emmi

Pubbl/distr/stampa

Milano : , : Springer Milan : , : Imprint : Springer, , 2014

ISBN

88-470-5477-X

Edizione

[1st ed. 2014.]

Descrizione fisica

1 online resource (227 p.)

Collana

Rare Diseases of the Immune System, , 2282-6505

Disciplina

616.97

Soggetti

Rheumatology

Dermatology

Internal medicine

Immunology

Pharmaceutical technology

Medical education

Internal Medicine

Pharmaceutical Sciences/Technology

Medical Education

Lingua di pubblicazione

Inglese

Formato

Materiale a stampa

Livello bibliografico

Monografia

Note generali

Description based upon print version of record.

Nota di bibliografia

Includes bibliographical references and index.

Nota di contenuto

Preface 1 Behçet syndrome -- Preface 2 Behçet's syndrome: the role of patient's Associations -- The numbers of Behçet: a rare disease -- Along the Old Silk Road -- Epidemiology of Behçet's syndrome -- Behçet's syndrome according to classical and population genetics -- Infections, autoimmunity and Behçet’s syndrome: what liaison -- Pathogenesis of Behçet's syndrome -- Muco-cutaneous involvement in Behçet's syndrome -- Neurological and neuro-psychological manifestation in Behçet's syndrome -- Ocular involvement and Behçet -- Muscle and articular manifestations in Behçet's syndrome -- Cardiovascular issues -- Intestinal Behçet Disease -- Audio vestibular involvement in Behçet's disease -- Pregnancy and Behçet's syndrome -- Pediatric Onset of Behçet's syndrome -- Differential Diagnosis -- Classification and Diagnosis Criteria for Behçet's Disease -- Prognosis and Disease Activity -- Old and New Treatment for Behçet's Disease -- Surgical management of Behçet's Disease.



Sommario/riassunto

Behçet's syndrome can reasonably be considered a unique entity among diseases of the immune system for several reasons: It has specific features and, uniquely among the immune system pathologies, represents a link between autoimmune diseases, systemic vasculitis, and autoinflammatory diseases. In addition, it is of interest to a variety of specialists, including immunologists, rheumatologists, dermatologists, and ophthalmologists, and requires a complex multidisciplinary approach. Many aspects need to be considered in a syndrome that presents a wide spectrum of symptoms and for which the therapeutic armamentarium is expanding significantly, with the development of new treatments, not least the so-called biologics. This book offers comprehensive coverage of the disease by some of the world’s leading experts in Behçet's syndrome from all the relevant specialties. Epidemiology, genetics, pathogenesis, organ system involvement, differential diagnosis, novel treatments, surgical management, and prognosis are just some of the topics addressed. Behçet's Syndrome: From Pathogenesis to Treatment will be an invaluable reference for a range of practitioners, researchers, and undergraduates or postgraduates interested in immunorheumatology, dermatology, and rare diseases.